| Bioactivity | 2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy. | ||||||||||||
| Invitro | 2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy[1]. The underlying biochemical defect involves isoleucine catabolism[2]. | ||||||||||||
| Name | 2-Methylsuccinic acid | ||||||||||||
| CAS | 498-21-5 | ||||||||||||
| Formula | C5H8O4 | ||||||||||||
| Molar Mass | 132.12 | ||||||||||||
| Transport | Room temperature in continental US; may vary elsewhere. | ||||||||||||
| Storage |
|