| Description | Trans-2-butene-1,4-dicarboxylic acid (3-Hexenedioic Acid) is a normal human unsaturated dicarboxylic acid metabolite with increased excretion in patients with Dicarboxylic aciduria caused by fatty acid metabolism disorders The urinary excretion of Trans-2-butene-1,4-dicarboxylic acid is increased in conditions of augmented mobilization of fatty acids or inhibited fatty acid oxidation. |
| Synonyms | trans-2-Butene-1,4-dicarboxylic Acid, 3-Hexenedioic Acid, trans-3-Hexenedioic Acid, β-Hydromuconic Acid, 反式-2-丁烯-1,4-二甲酸 |
| molecular weight | 144.13 |
| Molecular formula | C6H8O4 |
| CAS | 4436-74-2 |
| Storage | Powder: -20°C for 3 years | In solvent: -80°C for 1 year |
| Solubility | DMSO: 55 mg/mL (381.6 mM) |
| References | 1. Jin SJ, et al. Identification of isomeric unsaturated medium-chain dicarboxylic acids in human urine. J Lipid Res. 1989 Oct;30(10):1611-9. |